Anomalies associated with the development of the urinary tract, account for more than 35% of all congenital malformations in humans. In this case, cases where similar pathologies are asymptomatic and are determined only during puberty or pregnancy are not uncommon. The Frauleys syndrome is an anomaly of the kidneys of an innate nature, in which a cross between the anterior and posterior branches of the upper renal artery is formed. As a result, the normal functions of the organ are disrupted.
Its name was given to the syndrome by the name of the American urologist, who first described it. The article is suitable for the reasons, symptoms and treatment of the disease.
What it is?
As already mentioned, in the Freyle syndrome, the posterior and anterior branches of the renal artery cross. At the same time, partial compression of the upper parts of the pelvis or the ureteropelvic segment is possible. As a result of this function, the kidneys can be broken or completely lost. There is a probability of formation of stones, the appearance of arterial hypertension. Traces of blood can be found in the urine.
A similar anomaly arises in the course of embryogenesis of the vascular system of the kidneys, when it is possible to stop their development, but the preservation of structures.
Localizes the Freyle syndrome on the right and left, that is, it usually affects one kidney. In extreme cases, both organs can suffer. In this case, the syndrome can be accompanied by a defect in filling the upper group of cups and right-sided or left-sided pyeloectasia due to obstruction of the ureter.
Symptoms of the disease
There are some indications that indirectly indicate that the patient may have a Freyle syndrome. Symptoms are manifested by palpable pain in the lumbar region, renal colic, which are present in connection with secondary nephrolithiasis. In addition, there is an insignificant arterial hypertension, as well as macro- and microhematuria.
Diagnosis of the syndrome
The most difficult to clinically identify the Frauleys syndrome in small children, especially in infants. To establish the correct diagnosis, the method of dopplerography of the kidney vessels is used, and multispiral computed tomography is also used.
It is difficult for babies to carry out angiographic studies, so at present they are almost never used.
In addition to the above methods, patients are given the delivery of urine and blood tests, including sensitivity to drugs and flora. In addition, ultrasound is performed on the urinary system.
Treatment of this disease is prescribed only after a thorough comprehensive examination and confirmation of the diagnosis. Conservative method - hypotensive therapy - is used in rare cases. It is aimed, as a rule, to reduce the pressure in the event that it is increased. Also, a set of measures for the removal of secondary pyelonephritis and are involved in the prevention of urolithiasis.
However, the most reliable way to completely eliminate the Frauleys syndrome is treatment is not conservative, but surgical. During the operation, the doctor removes the crossing of the arteries in the kidneys and the pressure on them ceases.
In any case, patients (and especially babies) should register with a nephrologist and receive regular consultations, take the necessary tests, undergo ultrasound and radiographic examinations. In later life, the Frauleys syndrome may not manifest itself at all, the degree of discomfort depends on how much the renal pelvis is tightened. With a healthy lifestyle and lack of bad habits, patients may not feel any symptoms at all.
Pregnancy and the birth of a child with the syndrome of the maternity trauma take place only under the supervision of a specialist. As a rule, women with congenital malformations of the kidneys, which include this syndrome, are allowed to bear fruit only after the operation. The fact that the syndrome is often accompanied by an increase in blood pressure, pregnancy in this case is more difficult, sometimes it must be interrupted after 22 weeks.
But even after a successful operation and restoration of kidney function, a pregnant woman should be warned about this by her obstetrician-gynecologist. During the entire period of bearing the child, the patient must be under the control of the nephrologist, periodically take tests, undergo studies and, if necessary, be hospitalized.
Very often, exacerbation of kidney disease can occur at a period of 15-16 or 26-30 weeks. Symptoms include delayed discharge of urine, severe edema of the hands and feet, pain and discomfort during urination. In later terms complications are possible due to the rapidly growing uterus, which presses on the ureters. In the case of the appearance of such signs of a pregnant woman with the syndrome of Frauley urgent hospitalization is needed.
Childbirth with the syndrome of Freilley
Very often, kidney defects are an indication for caesarean section. However, the threat to the child in this case is insignificant.
For women with Freil's syndrome and other abnormalities of kidney development, there are specialized maternity hospitals, in which there are necessarily urologists and nephrologists, and a newborn child immediately after birth is subjected to a comprehensive examination.
So, in the article was considered such a kidney disease as the Frauley syndrome. Despite the fact that the anomaly is congenital, now it is successfully treatable, and patients after the operation can return to a normal lifestyle.