Anomalies associated with the development of the urinary tract, account for more than 35% of all congenital malformations in humans. In this case, cases where such pathologies are asymptomatic and are determined only during puberty or pregnancy are not uncommon. The Frauleys syndrome is an anomaly of the kidneys of an innate nature, in which a cross between the anterior and posterior branches of the upper renal artery is formed. As a result, the normal functions of the organ are disrupted.
The syndrome was named after the American urologist, who first described it. The article is suitable for the reasons, symptoms and treatment of the disease.
What it is?
As already mentioned, with the Freyle syndrome, the posterior and anterior branches of the renal artery cross. It is possible to partially squeeze the upper sections of the pelvis or the tuberculosis-ureteric segment. As a result of this function, the kidneys can be disturbed or completely lost. There is a possibility of formation of stones, the appearance of hypertension. Traces of blood can be found in the urine.
A similar anomaly arises during embryogenesis of the vascular system of the kidneys, when it is possible to stop their development, but the preservation of structures.
Localizes Freil's syndrome on the right and left, that is, it usually affects one kidney. In extreme cases, both organs can suffer. In this case, the syndrome may be accompanied by a defect in filling the upper group of cups and right-sided or left-sided pyeloectasia due to obstruction of the ureter.
Symptoms of the disease
There are some indications that indirectly indicate that the patient may have a Freyle syndrome. Symptoms are manifested by palpable pain in the lumbar region, renal colic, which are present in connection with secondary nephrolithiasis. In addition, there is a slight hypertension, as well as macro- and microhematuria.
Diagnosis of the syndrome
The most difficult to clinically identify the Frauleys syndrome in small, especially in infants. To establish the correct diagnosis, the method of dopplerography of the kidney vessels is used, and multispiral computed tomography is also used.
Babies are difficult to conduct angiographic studies, so at present they are almost not used.
In addition to the above methods, patients are given a surrender of urine and blood tests, including sensitivity to drugs and flora. In addition, ultrasound examination of the urinary system.
Methods of treatment
Treatment of this disease is prescribed only after a thorough comprehensive examination and confirmation of the diagnosis. Conservative method - hypotensive therapy - is used in rare cases. It is directed, as a rule, to reduce the pressure in the event that it is increased. Also, a set of measures for the removal of secondary pyelonephritis and are involved in the prevention of urolithiasis.
However, the most reliable way to completely eliminate the Frauleys syndrome is treatment is not conservative, but surgical. During the operation, the doctor removes the crossing of the arteries in the kidneys and the pressure on them ceases.
In any case, patients (and especially babies) should register with a nephrologist and receive regular consultations, take the necessary tests, undergo ultrasound and radiographic examinations. In later life, the Frauleys syndrome may not manifest itself at all, the degree of discomfort depends on how much the renal pelvis is pinched. With a healthy lifestyle and lack of bad habits, patients may not feel any symptoms at all.
Pregnancy and the birth of a child in the syndrome of the maternity trauma take place only under the supervision of a specialist. As a rule, women with congenital malformations of the kidneys, which include this syndrome, are allowed to bear fruit only after the operation. The fact that the syndrome is often accompanied by an increase in blood pressure, pregnancy in this case is more difficult, sometimes it should be interrupted after 22 weeks.
But even after a successful operation and restoration of kidney function, a pregnant woman should be warned about this by her obstetrician-gynecologist. During the entire period of bearing the child the patient must be under the control of the nephrologist, periodically take tests, undergo studies and, if necessary, be hospitalized.
Very often, exacerbation of kidney disease can occur at a period of 15-16 or 26-30 weeks. Symptoms are delayed urine, strong swelling of the hands and feet, pain and discomfort during urination. On later terms, complications are possible due to the rapidly growing uterus, which presses on the ureters. In the case of the appearance of such signs of a pregnant woman with the syndrome of Frauley urgent hospitalization is needed.
Childbirth in the syndrome of Freilley
Very often, kidney defects are an indication for caesarean section. However, the threat to the child in this case is insignificant.
For women in labor with Freil's syndrome and other anomalies of kidney development, there are specialized maternity hospitals, in which there are necessarily urologists and nephrologists, and a newborn child immediately after birth is subjected to a comprehensive examination.
So, in the article was considered such a kidney disease, as the Frauleys syndrome. Despite the fact that the anomaly is congenital, now it is successfully treatable, and patients after the operation can return to a normal lifestyle.